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Congenital Esophageal Stenosis in Children: From Etiology to Prognosis
소아의 선천성 식도 협착증
JKAPS 2018 Jun;24(1):1-4
Published online June 30, 2018;
Copyright © 2018 Korean Association of Pediatric Surgeons.

Soo-Hong Kim1, Hyun-Young Kim2
김수홍1, 김현영2

1Department of Pediatric Surgery, Pusan National University Children’s Hospital, Yangsan, 2Department of Pediatric Surgery, Seoul National University Children’s Hospital, Seoul, Korea
1부산대학교어린이병원 소아외과, 2서울대학교어린이병원 소아외과
Received March 5, 2018; Accepted April 13, 2018.
This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License ( which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
Congenital esophageal stenosis (CES) is a rare disease that has been reported to occur once in every 25,000 to 50,000 births. According to its etiology, CES is divided into 3 subtypes, tracheobronchial remnants (TBR), fibromuscular hypertrophy (FMH) and membranous diaphragm (MD). Symptoms begin at the weaning period and the introduction of solid food around 6 months with dysphagia and vomiting. Esophagography is first screening test and endoscopic ultrasonography plays important roles to diagnose subtypes deciding therapeutic plan. TBRs were generally treated with surgical resection and end-to-end anasotomosis, whereas FMH and MD had good response rate to endoscopic or radiologic guided dilatation. This article reviews the literature on the etiology, clinical course, diagnosis and management of CES including recent opinion.
Keywords : Congenital esophageal stenosis, Esophagus, Tracheobronchial remnants, Child


June 2018, 24 (1)